Kimura’s disease with recurrent bilateral lacrimal gland involvement in a male Japanese child successfully treated with cyclosporine A

Abstract Background Kimura’s disease (KD) is a rare chronic inflammatory of unknown etiology. Clinically, KD characterized by nodular subcutaneous masses, that are typically localized to the neck and head. Involvement lacrimal glands limbs uncommon seldom reported. Case presentation We report case 4-year-old Japanese boy presenting with bilateral upper eyelid swelling lesions peripheral eosinophilia. Based on clinical, histopathological, laboratory findings, patient was diagnosed KD. An itchy mass left arm developed at age 14 years. Treatment steroids effective. However, as were tapered after side effects, masses relapsed within few months. cyclosporine A then initiated, which led an improvement clinical features serial levels cytokines. Conclusions peculiar presentation. The responded well treatment A.